Les matieres fecales sont normalement propulsees au travers du colon par des muscles. Review the developmental etiology and pathogenesis of hirschsprung disease. Hirschsprung disease is a neonatal discovery in almost all cases, and the association of hirschsprung disease in adults with symptomatic intestinal malrotation is unusual. A 43yearold patient with a history of colectomy for colonic inertia and megadolichocolon was admitted to the carcassonne hospital. Please use one of the following formats to cite this article in your essay, paper or report. Introduction hirschsprung s disease hd is a malformation of the large intestine characterized by the absence of ganglion cells in submucosal and myenteric plexus, which produces a functional obstruction and dilatation proximal to the affected segment 1. Y mars 2009 slideshare utilise les cookies pour ameliorer les fonctionnalites et les performances, et egalement pour vous montrer des publicites pertinentes. A 43yearold patient with a history of colectomy for colonic inertia and megadolichocolon was admitted to the carcassonne hospital emergency. The technique considered as the golden standard for the diagnosis of hd is the absence of ganglion cells in a rectal biopsy specimen.
Congenitalmegacolon observation hv frederick ruysch. Ces muscles sont controles par des neurones speciaux appeles des cellules ganglionnaires. Elles necessitent le plus souvent une intervention chirurgicale pour corriger ces malformations. Hirschsprungs disease in the adolescent and adult is a. This combination delays diagnosis and can lead to mistake in surgical strategy.
Introduction dilatation colique en amont dune anomalie congenitale des plexus nerveux intra. Les symptomes sont une constipation severe et une distension abdominale. Le segment atteint est rectosigmoidien dans 80 % des cas, ou plus etendu. Hirschsprung s disease hd is rare in adults and it is thus often undiagnosed or misdiagnosed.
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